[Ebstein's anomaly: results of the conic reconstruction of the tricuspid valve].
نویسندگان
چکیده
OBJECTIVE To assess the results of a technical modification of tricuspid valvuloplasty in Ebstein's anomaly. METHODS From November 1993 to August 2002, 21 patients with Ebstein's anomaly of the tricuspid valve, with ages ranging from 20 months to 37 years (mean, 23 years), underwent a new technique of tricuspid valvuloplasty. This technique consisted of total or almost total detachment of the anterior tricuspid megaleaflet from the ventricular wall and valvular ring, transforming it into a cone, whose vertex remained fixed in the right ventricular tip, and the base was sutured to the tricuspid ring, after its plication, adjusting it to the size of the base of the cone (tricuspid ring), including the septal region. RESULTS One (4.7%) patient with cardiomyopathy caused by chronic hypoxia died in the hospital due to low cardiac output. The mean follow-up lasted 4 years, and the recent echocardiograms showed good morphology of the right ventricle and tricuspid valve with mild or minimal insufficiency in 18 patients and moderate insufficiency in 2 patients. In 2 of the 3 patients with an anomalous bundle, it could be located and sectioned during surgery. No atrioventricular block occurred. CONCLUSION The technique used was efficient in repairing tricuspid insufficiency and restoring right ventricular morphology, being applicable to all anatomic types of Ebstein's anomaly, except for Carpentier classification type D.
منابع مشابه
Echocardiographic spectrum of Ebstein's anomaly of the tricuspid valve.
Sixteen patients aged between one day to 18 years with Ebstein's malformation of the tricuspid valve were studied with ultrasound. The findings were compared with a group of 74 patients without Ebstein's malformation. Two features were considered specific for Ebstein's malformation: 1) ability to record the anterior tricuspid leaflet (ATL) farther to the left of the left sternal border than in ...
متن کاملEbstein's anomaly in adults: Modified cone reconstruction of the tricuspid valve is associated with promising outcomes.
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متن کاملگزارش یک مورد استروک در فردی جوان با آمبولی پارادوکس ناشی از وجودآنومالی ابشتاین
Introduction: Ebstein's anomaly (EA) is a rare congenital malformation of the tricuspid valve, often associated with PFO, which is present in 80-90% of patients & predisposes to para-doxical embolization. Case Report: The case described was a 30 year old female, in the post partum phase, (ten days after normal vaginal delivery) who was presented to the emergency department with seizure & Rt s...
متن کاملCorrected transposition of great vessels and Ebstein's anomaly of tricuspid valve. Echocardiographic findings.
A case is reported concerning echocardiographic findings in a patient with congenital corrected transposition of the great vessels and Ebstein's anomaly of the tricuspid valve. This presented an unusual opportunity to study atrioventricular valve closure in a patient in whom the Ebstein's malformation involved the systemic atrioventricular valve. The mitral to tricuspid valve closure interval w...
متن کاملImperforate Ebstein's anomaly of the tricuspid valve.
Sir: In the case report by Gerlis and Anderson (British Heart Journal, 1976, 38, 108), the authors are not correct in saying that there is no previous description of imperforate Ebstein's anomaly of the tricuspid valve. In 1973, we reported a case of Ebstein's malformation of the tricuspid valve with complete obstruction to the tricuspid valve orifice, i.e. atresia (Rao et al., 1973). The assoc...
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عنوان ژورنال:
- Arquivos brasileiros de cardiologia
دوره 82 3 شماره
صفحات -
تاریخ انتشار 2004